目的:探讨原发性系统性淀粉样变性并发凝血因子x缺乏的临床特征、发病机制及治疗方法。
Objective: to investigate the clinical feature, pathogenesis, and therapy of Primary systemic amyloidosis with acquired factor-X deficiency.
当淀粉样蛋白由免疫球蛋白轻链组成时,那么它就是“免疫细胞衍生性淀粉样变性”,当它来自于血清淀粉相关蛋白时,就是“反应性系统性淀粉样变性”。
When the amyloid protein is made up of immunoglobulin light chains, then it is "AL amyloid" and when it is derived from serum amyloid-associated protein, then it is "AA amyloid.
当淀粉样蛋白由免疫球蛋白轻链组成时,那么它就是“免疫细胞衍生性淀粉样变性”,当它来自于血清淀粉相关蛋白时,就是“反应性系统性淀粉样变性”。
When the amyloid protein is made up of immunoglobulin light chains, then it is "AL amyloid" and when it is derived from serum amyloid-associated protein, then it is "AA amyloid.
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