Pathological diagnosis: All were embryonal rhabdomyosarcoma.

The rhabdomyosarcoma showed signs of lobular solid mass within the renal parenchyma, pelvis or upper part of the ureter, with crescent low density subcapsular hematoma surrounding the kidney.

Conclusions: Embryonal rhabdomyosarcoma of the biliary tree, though rare, is the most common cause of biliary obstruction due to malignancy in childhood.